A Case of Mitochondrial Myopathy with Cardiac Involvement: Management in the Same Day Surgery Setting

During the last decade, disorders of the respiratory chain, socalled mitochondrial disorders, have emerged as a major clinical entity. Though Leigh’s disease, also known as Subacute Necrotizing Encephalomyelopathy, has been mostly reported in infancy and childhood, it is described in adults [1]. Leigh's disease is a myopathy causing degradation of motor skills with occasional cardiac involvement. Leigh’s disease occurs either because of the two possibilities: mutations in mitochondrial DNA or deficiency of X linked enzyme called pyruvate dehydrogenase [2]. Acquired Leigh’s disease as a result of spontaneous mutation also happens [3]. Reports of mitochondrial myopathies with cardiac involvement remain sparse [4].